- JIA patients suspected with macrophage activation syndrome usually have hyperferritinemia. （ ）
- Rheumatic diseases are defined as a large group of diseases that only affects the connective tissues of the body in the modern sense.（ ）
- In the ACR 1997 revised classification criteria for SLE，arthritis involves 3 or more peripheral joints.（ ）
- Kawasaki disease is a vasculitis that predominantly affects the large-size arteries.（ ）
- T cells and T cell subpopulations can be enumerated by flow cytometry recognizing CD antigens present on T cells ,usually CD19 or CD20. （ ）
- If the total immunoglobulin level less than 6 gram per liter or IgG less than 2 gram per liter, it indicates possible antibody defects.（ ）
- Myositis-associated autoantibodies are present specifically in patients with idiopathic inflammatory myopathies.（ ）
- The severity of pediatric SLE is notably worse than the typical course for adult onset SLE. （ ）
- Regular administration of IVIG, 400-600mg/kg,is suggested for hypogammaglobulinemia. （ ）
- Children with IgA vasculitis may experience recurrences.（ ）
- According to 10 warning signs of PID, if the child has recurrent, deep skin abscesses with a family history of primary immunodeficiency，we should pay attention to the possible presence of an underlying primary immunodeficiency disease of this child. （ ）
- The interval between streptococcal infection and the onset of the clinical manifestations of ARF is about 2 to 3 weeks. （ ）
- Antibiotic prophylaxis for patients, who did not have carditis with their initial episode of ARF, should continue until the patient reaches 18 year of age or until 3 years have elapsed since the last rheumatic fever attack.（ ）
- One of the characteristics of Kawasaki disease is bilateral conjunctival injection with exudate. （ ）
- The ulcers of the tongue and hard palate in SLE patients are typically painless. （ ）
- Which of the following are recommended as a first choice in the treatment of active moderate to severe juvenile localized scleroderma？（ ）
- Which of the following tests patients for T-cell defects?（ ）
- Which of the following are suggested in superficial circumscribed morphea？ （ ）
- Moderate to high-disease severity of Juvenile localized scleroderma includes（ ）
- Which of the following are associated with neonatal lupus？（ ）
- Which of the following tests patients for B-cell defects?（ ）
- Which of the following are right about replacement therapy of primary immunodeficiency disease?（ ）
- In juvenile systemic sclerosis，the skin goes through several phases，including: （ ）
- The pharmacological therapy of systemic lupus erythematosus includes ?（ ）
- Which of the following are included in the definition of Enthesitis-related Arthritis?（ ）
- Acute rheumatic fever is caused by（ ）.
- Which of the following is NOT a characteristic of Severe Combined Immunodeficiency? （ ）
- Which of the following is not a clinical feature of juvenile idiopathic arthritis? （ ）
- Which of the following is not the cause of SLE ? （ ）
- Hydroxychloroquine is an antimalarial drug important in the treatment of SLE and dermatomyositis. Which is the most significant potential adverse effect of hydroxychloroquine？（ ）
- A 1-month-old boy had recurrent hypocalcemic convulsions after birth. Physical examination: widening eye distance, micrognathism, increased muscle tone in extremities. X-ray examination showed no thymus shadow. Which of the following treatments should not be used in this child? （ ）
- The following drugs are generally used for the treatment of Kawasaki disease, except for（ ）
- What is the typical rash of SLE patients? （ ）
- Which test is the first choice to monitor for development of cardiovascular complication of Kawasaki disease. （ ）
- Which test is the first choice to do for a juvenile scleroderma patients who have abnormal pulmonary function tests? （ ）
- What's the difference between juvenile dermatomyositis and polymyositis？（ ）
- A 9-year- old boy was admitted to the hospital due to "fever for 2 weeks and joints pain for 1 week". The right shoulder joint was swollen and painful for 3 days and relieved by itself. Then the knees began swollen and painful. PE: T 38℃, slight congestion in pharynx, no special cardiopulmonary auscultation, swelling and tenderness of both knee joints with high local skin temperature, limitation of motion. The other joints are normal. Polycyclic red borders of erythema marginatum can be observed on the back. Laboratory tests: ESR 98mm/h, CRP 55mg/L. What is the most important test for a definitive diagnosis of this patient? （ ）
- A 6-year-old boy was admitted to hospital for "high fever for more than 1 month", accompanied by swelling and pain in the right wrist and left ankle. The rash became obvious when the body temperature rised. Antibiotic treatment was failed. PE: A congestive pink rash can be seen on the torso. Cervical lymphnodes enlargement. No special cardiopulmonary auscultation. The liver can be palpated 3cm below the costal, and spleen can be palpated 1cm below the costal. CBC: WBC 30×109/L, N 85%, Hgb 90g/L, CRP 95mg/L, ESR 120mm/h. ASO,blood culture,ANA were all normal. The most likely diagnosis is:（ ）
- Which of the following is not a primary immunodeficiency disease dominated by antibody deficiency? （ ）
- Which immunoglobulin can be transmitted to the fetus through the placenta? （ ）
- Regular administration of IVIG, 2g/kg,is suggested for hypogammaglobulinemia. （ ）
- About X-linked agammaglobulinemia, which of the following is NOT right? （ ）
- The immune system integrates 2 fundamental response mechanism，innate immunity and acquired immunity. （ ）
- T cells and T cell subpopulations can be enumerated by flow cytometry recognizing CD antigens, usually CD3, CD4, and CD8.（ ）
- About DiGeorge syndrome, which are right? （ ）
- Skin biopsies are needed for routine diagnosis of Juvenile Scleroderma. （ ）
- Pansclerotic morphea refers to oval or round shape lesions that are centrally indurated with a waxy, ivory color and a violaceous rim. （ ）
- Juvenile localized scleroderma is limited to the skin and not affects other organs.（ ）
- The signs of disease activity of Juvenile localized scleroderma include erythema and（ ）
- Raynaud phenomenon results from persistent vasospasm of peripheral arteries and arterioles, often in response to cold or stress. （ ）
- Kidney involvement is a significant cause of morbidity and mortality in both adult and pediatric patients with SLE. （ ）
- Children with SLE（cSLE）have more severe disease and more widespread organ involvement compared with adults.（ ）
- Kidney Involvement of SLE includes（ ）
- According to the ACR 1997 revised classification criteria for SLE，excluding other etiologies, presence of 4 of the 11 simultaneously establishes the diagnosis. （ ）
- Which autoantibody is of high specificity for SLE? （ ）
- The electromyography abnormalities are specific in juvenile dermatomyositis patients.（ ）
- Patients with juvenile dermatomyositis should not do any exercise. （ ）
- Idiopathic inflammatory myopathies (IIM) are a heterogenous group of diseases characterized by muscle weakness and inflammatory changes in skeletal muscle.（ ）
- The pathogenesis of juvenile dermatomyositis includes（ ）
- Which of the following are not included in the Bohan and Peter criteria of juvenile dermatomyositis?（ ）
- What are the organs often involved in anaphylactoid purpura?（ ）
- Infantile Acute Hemorrhagic Edema usually affect the skin and kidney.（ ）
- What is the complication that affect the prognosis in the acute phase of IgA vasculitis? （ ）
- IgA vasculitis is characterized by leukocytoclastic vasculitis and immunoglobulin A deposition in the medium vessels.（ ）
- Leukocytoclastic vasculitis with IgA deposition in affected tissues is very important in IgA vasculitis. Therefore, patients with IgA vasculitis need a biopsy to confirm the diagnosis.（ ）
- What's the pathogenesis of Kawasaki disease？（ ）
- What's the earliest symptoms of Kawasaki disease？（ ）
- Acute Kawasaki Disease recurs in 1–3% of cases.（ ）
- The duration of fever without treatment of Kawasaki Disease is usually longer than 4 weeks. （ ）
- Approximately 20–25% of untreated children develop coronary artery abnormalities, whereas 内容已经隐藏，点击付费后查看
- About oligoarthritis，which of the following is not true? （ ）
- The definition of juvenile idiopathic arthritis requires the duration of arthritis to be?（ ）
- Which of the following manifestations can occur in juvenile idiopathic arthritis patients? （ ）
- ANA seropositivity is associated with increased risk of chronic uveitis in JIA.（ ）
- Juvenile idiopathic arthritis is a leading cause of acquired disability and blindness in the pediatric age group. （ ）
- What does the prognosis of rheumatic fever mainly depend on？（ ）
- Which of the following is not the characteristic of rheumatoid arthritis in acute rheumatic fever? （ ）
- The latency period between the inciting streptococcal pharyngitis and the onset of clinical signs of chorea is about 2 to 4 months, and sometimes as long as 12 months. （ ）
- Most of acute rheumatic fever occur in children younger than 5 years of age.（ ）
- The subcutaneous nodules of acute rheumatic fever are usually located on the flexor surfaces of the joints.（ ）
- An autoimmune response is an abnormal immune response that targets its own tissues and cells.（ ）
- Common symptoms of rheumatic diseases include （ ）:
- The ANA test result can not be positive in normal children. （ ）
- Which of the following statements about autoantibodies is not right?（ ）
- The goal of treatment of rheumatic diseases is to cure the disease，no matter what the drug we use.（ ）
答案:对
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答案:对
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答案:对
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